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Weekly Case

종결 Case No. 691 2024-07-01~2024-07-31
출제자 : 이명환 Hit : 426
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Period 2024-07-01~2024-07-31
Diagnosis Neuro-Behcet disease
Gender
  • M
  •  
  • F
Age 61
Clinical information F/61,
C.C: Headache, Diplopia, General weakness
History: 10년 전부터 oral, genital ulcers로 피부과 f/u 중
Discussion Neuro-Behcet disease
• Chronic, idiopathic, relapsing-remitting, multisystem, inflammatory vascular disease
• Recurrent oral/genital ulcer, aphthous stomatitis, uveitis and iridocyclitis, multiple arthralgia
• 20-25% involve CNS: Neurobehcet disease

Image finding
 Parenchymal lesion
 meningoencephalitis
 Brainstem (esp. cerebral peduncle, 50%)> thalamus, basal ganglia> cerebral WM, spinal cord
 T2/FLAIR hyperintensity in midbrain +/- mass effect
 Mild to moderate patchy enhancement
 Chronic – lacune, brainstem & cerebellar atrophy
 Nonparenchymal lesion
 Dural sinus or cortical venous thrombosis >> arterial occlusion, aneurysm
Correct answer

Correct Answer

  • 박혜주 순천향대학교 부천병원
  • 김찬순 계명대학교 동산의료원
  • 도윤아 분당서울대학교병원
  • 윤정택 경희대학교병원
  • 김지환 양산부산대학교병원
  • 홍혁기 서울의료원
  • 이진영 동국대학교 일산병원
  • 김신영 양산부산대학교병원
  • 김동일 경희대학교병원
  • 조서범 연세대학교 세브란스병원

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