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Weekly Case

종결 Case No. 563 2020-08-01~2020-08-31
출제자 : 강경미 Hit : 606
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Period 2020-08-01~2020-08-31
Diagnosis Creutzfeldt-Jakob Disease
Gender
  • M
  •  
  • F
Age 66
Clinical information M/66
Dizziness, gait disturbance (3WA)
진단은?
Discussion • Rapidly progressing, fatal, potentially transmissible dementia caused by a prion.
• 4 CJD types: sporadic (sCJD) (85%), genetic/familial (gCJD) (5-15%), iatrogenic (iCJD) (2-5%), variant ("mad cow" disease, vCJD) (< 1%)
• MR with DWI is the imaging procedure of choice
• FLAIR hyperintensity or restricted diffusion in the caudate nucleus and putamen or in at least two cortical regions (temporal-parietal-occipital "cortical ribboning")

Correct answer

Correct Answer

  • 문경일 전남대학교병원
  • 변성환 순천향대학교 부천병원
  • 이진영 ----
  • 최규성 서울대학교병원
  • 윤선근 가톨릭대학교 성빈센트병원

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