| Period | 2020-08-01~2020-08-31 |
|---|---|
| Diagnosis | Creutzfeldt-Jakob Disease |
| Gender |
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| Age | 66 |
| Clinical information | M/66 Dizziness, gait disturbance (3WA) 진단은? |
| Discussion | • Rapidly progressing, fatal, potentially transmissible dementia caused by a prion. • 4 CJD types: sporadic (sCJD) (85%), genetic/familial (gCJD) (5-15%), iatrogenic (iCJD) (2-5%), variant ("mad cow" disease, vCJD) (< 1%) • MR with DWI is the imaging procedure of choice • FLAIR hyperintensity or restricted diffusion in the caudate nucleus and putamen or in at least two cortical regions (temporal-parietal-occipital "cortical ribboning") |
| Correct answer |
Correct Answer
Semi-Correct Answer |