| Period | 2019-09-01~2019-09-30 |
|---|---|
| Diagnosis | Neurobehcet disease |
| Gender |
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| Age | 48 |
| Clinical information | 48세 남환 Hx> 2일전 발생한 gaze palsy 주소로 내원하여 시행한 MR 이다. 진단은? |
| Discussion | Neurobehcet disease - Chronic idiopathic replasing-remitting multisystem inflammatory vascular disease - 20-25% patients suffer from CNS involvement. - affects young adult (male predominance) - Parenchymal neurobehcet : meningoencephalitis with brainstem, hemisphere, spinal cord lesion - No parenchymal neurobehcet : dural sinus thrombosis, arterial occlusion, and/or aneurysm Imaging - Brain stem involvement (cerebral peduncle), 50% - Thalamus and basal ganglia (2nd m/c) - Cicular, linear, crescent, or irregular T2/FLAIR hyperintense foci - Minimal mass effect (but significant mass effect can occur in acute phase) - Mild to moderate patchy enhancement |
| Correct answer |
Correct Answer
Semi-Correct Answer |