| Period | 2019-05-01~2019-05-31 |
|---|---|
| Diagnosis | Hirayama disease |
| Gender |
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| Age | 22 |
| Clinical information | M/22 임상정보: Right hand weakness, 3 yrs ago. 진단은? |
| Discussion | # Hirayama disease - Sporadic juvenile muscular atrophy of the upper limb affects young men predominantly. - Insidious unilateral or asymmetric bilateral muscular atrophy and weakness of the hand and forearm without sensory or pyramidal sign - MRI findings Localized lower cervical cord atrophy Asymmetric cord flattening Parenchymal changes in lower cervical cord Loss of attachment between the posterior dural sac and subjacent lamina On Flexion MRI, Forward migration of the wall of dura mater Enlarged posterior epidural space On CE-T1WI, hyperintense, cresenttic epidural mass showing curvilinear flow voids and iniform enhancement congestion of posterior internal vertebral venous plexus |
| Correct answer |
Correct Answer
Semi-Correct Answer |