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Weekly Case

종결 Case No. 418 2016-08-01~2016-08-31
출제자 : 강경미 Hit : 427
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Period 2016-08-01~2016-08-31
Diagnosis Primary CNS angiitis
Clinical information F/50
Dysarthria, 1주일전부터
진단은?
Discussion
Primary arteritis confined to intracranial CNS
No evidence of secondary (systemic) vasculitis

Imaging findings
- Angiography : Ectasia and stenosis reffered to as ‘beading’
But to small to detect!!
- CT : Secondary signs, such as ischemia or infarction
Patchy areas of enhancement
- MRI : Tissue ischemia or necrosis d/t narrowed and thrombosed vessels
Tumor like lesion without mass effect
 T1WI : Multifocal deep GM & subcortical WM hypointensities
 T2WI & FLAIR : Multifocal deep GM & subcortical WM hyperintensities
 GRE : show dark signals indicating petechial hemorrhage
Reference>
Am J Neuroradiol 2002;23:1561–1563
Arch Neurol. 2009;66(6):704-709
Diagnostic Imaging: Brain, Osborn et al, Amirsys, 2009
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