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Case No. 330
2014-03-03~2014-03-31
출제자 : 정원상
Hit : 342
| Period | 2014-03-03~2014-03-31 |
|---|---|
| Diagnosis | Neurocutaneous melanosis |
| Clinical information | M/9 Intermittent headache and vomiting, gait disturbance |
| Discussion | Neurocutaneous melanosis Diagnosis of Neurocutaneous melanosis (NCM) - Large or multiple congenital melanocytic nevi - benign or malignant proliferation melanocyte at leptomeninges Skin lesion of Neurocutaneous melanosis - 2.5 – 11% in patients with giant congenital nevus - 2/3 pts : giant melanocytic nevus in lumbosacral region - 1/3 pts : small numerous melanocytic nevus without large nevus - Large, congenital melanocytic nevi in a posterior axial location with ‘satellite’ melanocytic nevi greater risk for the development of neurocutaneous melanosis Neurologic symptoms - usually occur around age 2 - progressive and rapid fatal neurologic symtoms - 2/3 patients show symptoms of hydrocephalus - spinal cord involvement : myelopathy, radiculopathy, bowel or bladder dysfunction Treatment and prognosis - No curative treatment |
| Correct answer |
Correct AnswerSemi-Correct Answer |